다발성 유아기 흑색 신경외배엽성 종양의 치험례
Multicentric melanotic neuroectodermal tumor of infancy: a case report
최병환, 박수원, 장수미, 박봉찬, 손한나, 손장호, 성일용, 김종렬, 조영철,
소속 상세정보
최병환 ( Choi Byoung-Hwan ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
박수원 ( Park Su-Won ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
장수미 ( Jang Soo-Mi ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
박봉찬 ( Park Bong-Chan ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
손한나 ( Son Han-Na ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
손장호 ( Son Jang-Ho ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
성일용 ( Sung Iel-Yong ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
김종렬 ( Kim Jong-Ryoul ) - 온병원 구강악안면외과
조영철 ( Cho Yeong-Cheol ) - 울산대학교 의과대학 울산대학교병원 구강악안면외과학교실
KMID : 0355620100360050434
Abstract
A melanotic neuroectodermal tumor of infancy (MNTI) is a uncommon osteolytic pigmented neoplasm that primarily affects the jaws of newborn infants. Most patients (> 90%) present with the tumor in the first year of life. Approximately 65% form in the maxilla, 11% in the mandible, 5% in the brain and elsewhere. MNTI is normally benign, but up to 15% may recur and a few have metastasized. Approximately 200 cases of MNTI have been reported but only 2 of them presented as multifocal. A case of MNTI in a 7 month old boy was encountered. The chief complaint was maxillary anterior ridge swelling. The incisional biopsy findings were MNTI. Two months after the first operation, mild swelling of another site was observed. The infant was examined periodically since undergoing two procedures with no recurrence. This case demonstrates the possibility of a multicentric MNTI. We report a multicentric MNTI with a review of the relevant literature.
키워드
Melanotic neuroectodermal tumor of infancy(MNTI);Multicentric
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